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Rare Diseases of the Respiratory System

Rare Diseases of the Respiratory System

  • This book will be published in June 2023. It will be available for pre-order in April 2023.

    Edited by Thomas Wagner, Marc Humbert, Marlies Wijsenbeek-Lourens, Michael Kreuter and Helge Hebestreit

    Contents list (subject to change)
    1. How to identify rare diseases of the respiratory system
    2. Differential diagnosis of lung diseases, including pseudo-tumours and reciprocal mimics of neoplastic and non-neoplastic pulmonary disorders

    Rare diseases of the lung interstitium
    4. Interstitial lung diseases
    5. Rare interstitial lung diseases of environmental origin, including hypersensitivity pneumonitis and occupational exposures
    6. Amyloidosis and the lung
    7. Multiple cystic lung diseases including lymphangioleimyomatosis

    ​​​​​​​Rare disease of the airways or alveoli​​​​​​​​​​​​​​
    8. Bronchiolitis
    ​​​​​​​9. Alveolar proteinosis
    ​​​​​​​10. Primary ciliary dyskinesia
    ​​​​​​​11. Cystic fibrosis and other ion channel related diseases
    12. Non-cystic fibrosis bronchiectasis
    ​​​​​​​13. Alpha-1-antitrypsin deficiency and other rare forms fo emphysema

    Pulmonary vascular diseases
    14. Pulmonary arterial hypertension
    15. Chronic thromboembolic pulmonary hypertension
    16. Pulmonary hypertension in orphan lung diseases
    17. Hepatopulmonary syndrome: a liver-induced oxygenation defect

    Rare lung diseases in systemic inflammatory disorders
    18. Systemic inflammatory diseases with rare lung involvement (including Behçet's disease and Takayasu's arteriitis)
    19. Granulomatosis with polyangiitis and other pulmonary haemorrhage syndromes
    20. Eosinophilic granulomatosis with polyangiitis and other vasculitis
    ​​​​​​​21. Idiopathic eosinophilic pneumonias
    ​​​​​​​22. Sarcoidosis
    ​​​​​​​23. Granulomatous lymphocytic interstitial lung disease

    Other rare lung diseases
    24. Thoracic endometriosis and catamenial pneumothorax
    ​​​​​​​25. Chronic lung allograft dysfunction
    26. Malformations and idiopathic tracheopathies
    ​​​​​​​27. Rare diseases of the respiratory drive
    28. Mesothelioma and other rare tumours of the respiratory system

    ISBN: 9781849841665

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    Delivery times (estimated) are as follows:
    Europe: 7-15 business days from date of despatch. 
    Rest of the World: 20-25 business days from date of despatch.
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