Pulmonary Manifestations of Systemic Diseases

Special offer to accompany the ERS course on Interstitial Lung Diseases – €10 off when you order before 1 May 

Edited by Wim A. Wuyts, Vincent Cottin, Paolo Spagnolo and Athol U. Wells
Interest in interstitial lung diseases (ILDs) has risen in recent years. A large volume of basic and clinical research has increased our understanding of the pathogenesis of idiopathic pulmonary fibrosis (IPF) and non-IPF fibrotic ILDs. The ILD field is now evolving rapidly, with major implications for practical management.

This Monograph provides expert clinical guidance on these difficult diseases, which will be helpful to both respiratory and nonrespiratory physicians alike. The initial chapters consider diagnostic issues, pulmonary function tests and techniques that are currently in development. The book then goes on to cover a variety of pulmonary manifestations of very different disease entities, such as connective tissue diseases, systemic vasculitis and much more. 

Contents list 

1. Multidisciplinary approach to systemic diseases: benefits for diagnosis and management of complex disorders
2. Pulmonary function tests in multisystem disorders: prejudices and pitfalls
3. Quantitative CT analysis in ILD and the use of artificial intelligence on imaging of ILD

Connective tissue diseases
4. Rheumatoid arthritis
5. Inflammatory myopathies
6. Systemic sclerosis
7. Systemic lupus erythematosus, Sjögren syndrome and mixed connective tissue disease
8. Antiphospholipid syndrome
9. Interstitial pneumonia with autoimmune features 

Systemic vasculitides
10. Microscopic polyangiitis and granulomatosis with polyangiitis
11. Diffuse alveolar haemorrhage
12. Eosinophilic granulomatosis with polyangiitis
13. Takayasu arteritis and Behçet disease

Other diseases with extrathoracic involvement
14. Airway and lung involvement in inflammatory bowel disease
15. Liver disease: hepatopulmonary syndrome and portopulmonary hypertension 
16. Neuromuscular diseases
17. Amyloidosis
18. Trafficking and lysosomal storage disorders 
19. Haematological disorders and bone marrow transplant recipients 
20. Histiocytic disorders
21. Immunodeficiency
22. Telomere syndrome 
23. Sarcoidosis: pulmonary manifestations and management

Print ISBN: 978-1-84984-111-5
eISBN: 978-1-84984-112-2
EPUB ISBN: 978-1-84984-113-9